An adult patient with the Proteus syndrome sustained a grade III splenic laceration after falling off a horse. Clinical features of this rare disorder include subcutaneous and visceral hamartomatous tumours. The patient also suffered from chronic intravascular coagulation associated with extensive haemangiomatosis (Kasabach-Merritt syndrome). Considering the visceral anomalies and abnormal coagulation, a non-operative approach was preferred despite considerable transfusion requirement, and the patient successfully underwent embolisation of the splenic artery. This is the first reported case of splenic injury in a patient with Proteus syndrome.
CITATION STYLE
Ceelen, W., De Waele, J., Kunnen, M., & De Hemptinne, B. (1997). Non-operative management of a splenic laceration in a patient with the Proteus syndrome. Journal of Accident and Emergency Medicine, 14(2), 111–113. https://doi.org/10.1136/emj.14.2.111
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