Epidermólisis ampollosa de la unión: Implicación oral. A propósito de un caso

Abstract

Epidermolysis bullosa is the name given to a group of rare genetically determined diseases of de skin and mucosal membranes, characterized by the development of blisters and vesicles in response to minor trauma. Is characterized by extensive phenotypic variability with considerable morbidity and mortality. Epidermolysis bullosa is classified into distinct subtypes depending on the location of blistering within the cutaneous dermoepidermal basement membrane zone.