Primary rhabdomyosarcoma of the diaphragm: case report and literature review.

16Citations
Citations of this article
6Readers
Mendeley users who have this article in their library.

Abstract

The authors report a case of primary rhabdomyosarcoma of the diaphragm, an extremely rare presentation with only 14 cases reported in the literature. An 18-year-old male presented 2 spontaneous occurrences of pneumothorax. Computed tomography and magnetic resonance showed a tumoral mass on the right diaphragmatic surface, and after biopsy, the diagnosis was compatible with spindle cell rhabdomyosarcoma. Because the visceral pleura was invaded by the tumoral mass, a right pleuropneumonectomy was performed. The patient received adjuvant chemotherapy, and there was no evidence of disease 15 months after the operation. Based on the Intergroup Rhabdomyosarcoma Study Group (IRSG) criteria, which consider the extent of the disease and its surgical resectability, rhabdomyosarcomas can be classified into 4 groups. In clinical group I, which was the classification of our patient, the tumor is localized and completely resectable, which implies a good prognosis. Rhabdomyosarcoma is a rare tumor, and a good outcome may result if it is completely resected.

Cite

CITATION STYLE

APA

Medeiros, C. W. de L., Kondo, W., Baptista, I., Vizzotto, A. O., Noronha, L. de, & Hakim Neto, C. A. (2002). Primary rhabdomyosarcoma of the diaphragm: case report and literature review. Revista Do Hospital Das Clínicas. https://doi.org/10.1590/S0041-87812002000200004

Register to see more suggestions

Mendeley helps you to discover research relevant for your work.

Already have an account?

Save time finding and organizing research with Mendeley

Sign up for free