Isolated congenital tracheal stenosis: A rare and deadly condition

Abstract

Introduction: Congenital tracheal stenosis (CTS) is a serious and rare condition. In most cases, CTS is associated with cardiopulmonary abnormalities; however, isolated CTS is present in 10%–30% of patients. The severity of the disorder is dependent on the symptoms, which correlate with the CTS classification. Case presentation: We discuss our findings in an infant who presented with severe respiratory compromise where incidental intra-operative findings revealed CTS with no cardiopulmonary abnormalities. Because of a lack of resources in the emergency department, we created a tracheostoma and inserted an endotracheal tube. Conclusion: The main aim in treating CTS is to secure the airway and provide sufficient oxygen.