Poland syndrome

Abstract

Poland syndrome is a congenital anomaly with unilateral agenesis or hypoplasia of the pectoral muscles, deformity of the anterior chest wall and upper extremity anomalies. In patients with Poland syndrome, varying rates of breast asymmetry, from hypomastia to amastia, accompany. It is observed that the incidence of dextrocardia is increased in patients with left-sided Poland syndrome. Vital lung capacity may be reduced due to anterior chest wall deformity. This syndrome is thought to be due to a temporary impairment of circulation in the arteria subclavia or any of its branches or hypoplasia of these vessels during the development of the upper extremities in the intrauterine period. We aimed to emphasize the characteristics of Poland syndrome in a 26-year-old female case. On physical examination, pectus excavatum deformity was observed besides the absence of left pectoralis major and minor muscles with plica axillaris anterior. In terms of congenital or acquired pathologies that may accompany, the cases should be evaluated clinically in detail and followed up.