Combined double chambered right ventricle and discrete subaortic stenosis

Abstract

Nine cases of combined double-chambered right ventricle (DCRV) and discrete subaortic stenosis (DSAS) are presented. A review of 1077 consecutively catheterized patients indicates an association of these 2 uncommon anomalies 9 times greater than expected. One or both obstructive lesions may be hemodynamically significant and require surgery. Whenever DCRV and DSAS is suspected or identified, the cardiac catheterization should include studies of both the right and left ventricles.