The pulmonary atresia with ventricular septal defect is a high-complex severe and unusual cyanotic congenital heart disease, characterized by the lack of connection between the right ventricle and the pulmonary arteries; it coexists with a ventricular septal defect. The blood supply of the lungs is possible due to the presence of the patent ductus arteriosus or the major aortopulmonary collaterals. The severity of this heart defect is determined by the extreme variation of the interruption level from the right ventricle to the pulmonary vessel territory, and the anatomy of the blood supply to the lungs that will determine the surgical management strategy. © 2013 Sociedad Española de Cirugía Torácica-Cardiovascular.
Centella Hernández, T., Stanescu, D., & Stanescu, S. (2014). Atresia pulmonar con comunicación interventricular. Cirugia Cardiovascular, 21(2), 132–137. https://doi.org/10.1016/j.circv.2014.02.003