Multiple odontogenic keratocysts associated with Gorlin-Goltz syndrome

Abstract

Gorlin-Goltz syndrome or Nevoid basal cell carcinoma syndrome is an autosomal dominant disorder with a predisposition to cancer. Features like basal cell carcinoma, odontogenic keratocysts, calcifi cation of falx cerebri, bifi d ribs, pits on palms and soles and hypertelorism are evident. A case of this rare disease seen on a 13 year old female patient is presented here, where multiple odontogenic keratocysts were causing disfi gurement of the lower jaw as well as displacement and malocclusion of the lower teeth.