Systemic-pulmonary arteriovenous fistulae with pulmonary hypertension

Abstract

Background: Arteriovenous (AV) fistulae is an extremely rare disease of vascular malformation that involves fistulae formation between the systemic and pulmonary AV systems. Case representation: This case report describes a rare systemic-pulmonary AV fistulae of congenital origin, accompanied by pulmonary hypertension, as determined by aortic angiography and echocardiography. Conclusion: Characteristics, diagnosis, and therapeutic approaches of this rare abnormality are explored.