A 33-year old female with a background of Eisenmenger syndrome secondary to multiple congenital muscular ventricular septal defects (VSD) was admitted with a recent history of frequent intermittent palpitations. It was noted that she had an independent accelerated idioventricular rhythm (AIVR), with rates varying between 85-110bpm, which exhibited a repetitive grouped beating pattern. Although generally perceived as benign, in this case this rhythm was drug refractory, was associated with significant compromise to cardiac filling and output and progressed to haemodynamically intolerable sustained ventricular tachyarrhythmia. Successful ablation was performed at the inferior aspect of the residual VSD, from within the Purkinje network.
Honarbakhsh, S., Suman-Horduna, I., Mantziari, L., & Ernst, S. (2013). Grouped beating in Eisenmenger: Successful localization and ablation of an accelerated idioventricular rhythm from within the Purkinje system. Indian Pacing and Electrophysiology Journal, 13(3), 126–130. https://doi.org/10.1016/S0972-6292(16)30631-3