Metastatic Ewing's sarcoma/PNET of kidney in 40 year old patient

3Citations
Citations of this article
7Readers
Mendeley users who have this article in their library.

Abstract

INTRODUCTION: Primary renal Ewing sarcoma/PNET is an uncommon and very aggressive tumor. PRESENTATION OF CASE: We report the case of a young woman who underwent nephrectomy for a renal mass from unknown etiology. Histologic analysis found small tumoral cells in rosette formation, and immunohistochemical staining was positive for CD99, and focally positive for vimentin and Protein S- 100. A post operative abdominal computed tomography (CT) scan revealed a residual renal processus with hepatic wounds and abdominal metastatic nodes. After 6 cycles of chemotherapy including Vincristine, Doxorubicin, Cyclophosphamide, the response was considered as good. DISCUSSION: Ewing's sarcoma/PNET of kidney is a member of the family of small round cell tumors and it should be differentiated from Wilms tumor, neuroblastoma, rhabdomyosarcoma and lymphoblastic lymphoma. The principle management of its treatment have been extrapolated from the treatment of osseous Ewing sarcoma of bone. CONCLUSION: Despite aggressive treatment, primary renal Ewing sarcoma/PNET has a poor prognosis. It requires a multidisciplinary approach including oncologists, urologists and radiation oncologists. © 2012 Surgical Associates Ltd. Published by Elsevier Ltd. All rights reserved.

Author supplied keywords

Cite

CITATION STYLE

APA

Kairouani, M., Mokrim, M., Mellas, N., Khennoussi, B., El M’rabti, H., Boutayeb, S., & Errihani, H. (2012). Metastatic Ewing’s sarcoma/PNET of kidney in 40 year old patient. International Journal of Surgery Case Reports. Elsevier Ltd. https://doi.org/10.1016/j.ijscr.2011.12.009

Register to see more suggestions

Mendeley helps you to discover research relevant for your work.

Already have an account?

Save time finding and organizing research with Mendeley

Sign up for free