Monozygotic twins with Marfan's syndrome and ascending aortic aneurysm

  • H.J. R
  • T.F. C
  • E.F. R
  • et al.
N/ACitations
Citations of this article
3Readers
Mendeley users who have this article in their library.

Abstract

Marfan's syndrome is a hereditary connective tissue disease, in which cardiovascular abnormalities (especially aortic root dilatation) are the most important cause of morbidity and mortality. In this report, we describe two 24-year-old twins, with a history of surgery for lens subluxation and severe cardiovascular manifestations secondary to Marfan's syndrome. One of the twins suffered a type A aortic dissection, which required replacement of the ascending aorta, and the other twin had an aneurysmal dilatation of the ascending aorta (46 mm) and was prescribed medical treatment with atenolol and periodic controls to detect the presence of a critical diameter (50 mm) that would indicate the need for prophylactic surgery. © 2006 The European Society of Cardiology.

Cite

CITATION STYLE

APA

H.J., R., T.F., C., E.F., R., B., R., J.A., L., V.P., P., & S.M., B. (2007). Monozygotic twins with Marfan’s syndrome and ascending aortic aneurysm. European Journal of Echocardiography. Oxford University Press (Great Clarendon Street, Oxford OX2 6DP, United Kingdom). Retrieved from http://ovidsp.ovid.com/ovidweb.cgi?T=JS&PAGE=reference&D=emed11&NEWS=N&AN=46969889

Register to see more suggestions

Mendeley helps you to discover research relevant for your work.

Already have an account?

Save time finding and organizing research with Mendeley

Sign up for free