Objectives. We sought to assess the results after bidirectional cavopulmonary shunt (BCPS) in infants <6 months old and to identify risk factors for poor outcome. Background. Although BCPS is a well established procedure for the palliation of patients with a single-ventricle heart, there have been very few reports of outcomes after BCPS in young infants. Methods. Since 1990, 42 infants between 0.8 and 6.0 months of age (mean [±SD] 3.7 ± 1.4) have undergone BCPS for primary (n = 16) or secondary (n = 26) palliation of tricuspid atresia (n = 13), hypoplastic left heart syndrome (n = 10) or other forms of functional single-ventricle heart (n = 19). Accessory pulmonary blood flow was included in 18 patients. Preoperative and perioperative data were gathered on retrospective review of patient records, and follow-up was conducted by means of direct physician contact or record review. Results. The overall hospital mortality rate, including that associated with reoperations, was 4.8% (2 of 42 patients). Seven patients (17%) required reoperation related to the BCPS or pulmonary blood flow in the early postoperative period: Procedures included take-down of the BCPS in four patients, with one early death, and procedures to decrease pulmonary blood flow in three patients. Age <1 month correlated significantly with early death and with early failure of the BCPS (death or take-down). Follow-up of the 37 patients discharged with intact BCPS was obtained at a mean ± SD of 14.3 ± 11.3 months postoperatively, during which time three patients died (at 6.5 ± 2.5 months). The 2-year actuarial survival rate for patients undergoing BCPS at <6 months of age was 86%. Overall freedom from death or take-down (including early and late events) was significantly lower in patients <2 months old than in those >2 months old. Four patients have undergone successful Fontan completion (18.3 ± 2.9 months postoperatively), and one patient whose BCPS was taken down subsequently underwent successful restoration of a BCPS. Conclusions. Outcomes after BCPS in young infants are comparable to those in older infants and children. However, our current preference is to defer this procedure until after 2 months of age.
Reddy, V. M., McElhinney, D. B., Moore, P., Haas, G. S., & Hanley, F. L. (1997). Outcomes after bidirectional cavopulmonary shunt in infants less than 6 months old. Journal of the American College of Cardiology, 29(6), 1365–1370. https://doi.org/10.1016/S0735-1097(97)00068-5