Klippel-Trenaunay syndrome (KTS) is a rare complex vascular congenital malformation.The characteristic triad is an association of a cutaneous capillary angioma of a limb, venous malformations, and hypertrophy of soft tissue and/or bone.Diagnosis is essentially clinical.Work-up of the lesion may involve noninvasive imaging: Doppler ultrasound, standard radiography, or magnetic resonance imaging (MRI).The presence of arteriovenous malformations is sought by clinical examination or ultrasound: they rule out a diagnosis of KTS.Management is multidisciplinary and involves especially venous control and orthopedic management of unequal limb lengths. © 2010 Elsevier Masson SAS.
Samimi, M., & Lorette, G. (2010, April). Syndrome de Klippel-Trenaunay. Presse Medicale. https://doi.org/10.1016/j.lpm.2009.10.016