Bicuspid aortic valve (BAV) disease is the most common form of congenital heart disease, affecting 1-2% of the population. Only 20% of patients will maintain normal valve function throughout their life and more than 30% of patients will develop serious morbidity. It is a highly heritable condition, with transmission likely to be autosomal dominant. Patients with BAV have a 10-fold risk of aortic dissection when compared to the normal population. Management of BAV associated aortopathy represents a significant clinical challenge. © 2008 Australasian Society of Cardiac and Thoracic Surgeons and the Cardiac Society of Australia and New Zealand.
Vallely, M. P., Semsarian, C., & Bannon, P. G. (2008, October). Management of the Ascending Aorta in Patients with Bicuspid Aortic Valve Disease. Heart Lung and Circulation. https://doi.org/10.1016/j.hlc.2008.01.007