Non-invasive ventilation usage and adherence in children and adults with Duchenne muscular dystrophy: A multicenter analysis

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Abstract

Introduction/Aims: Non-invasive ventilation (NIV) is routinely prescribed to support the respiratory system in Duchenne muscular dystrophy (DMD) patients; however, factors improving NIV usage are unclear. We aimed to identify predictors of NIV adherence in DMD patients. Methods: This was a multicenter retrospective analysis of DMD patients prescribed NIV and followed at (1) The Hospital for Sick Children, Canada; (2) Rady Children's Hospital San Diego, USA; and (3) University of California San Diego Health, USA, between February 2016 and October 2020. The primary and secondary outcomes were 90-day period NIV adherence and clinical and socioeconomic predictors of NIV adherence. Results: We identified 59 DMD patients prescribed NIV (mean ± SD age = 20.1 ± 6.7 y). Overall, percentage of nights used, and average nightly usage, were 79.9 ± 31.1% and 7.23 ± 4.12 h, respectively. Compared with children, adults had higher percentage of nights used (92.9 ± 16.9% vs. 70.4 ± 36.9%; P

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Hurvitz, M., Sunkonkit, K., Defante, A., Lesser, D., Skalsky, A., Orr, J., … Bhattacharjee, R. (2023). Non-invasive ventilation usage and adherence in children and adults with Duchenne muscular dystrophy: A multicenter analysis. Muscle and Nerve, 68(1), 48–56. https://doi.org/10.1002/mus.27848

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