Intranasal dermoplasty for epistaxis in a patient with hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu disease): A case report

Abstract

Hereditary hemorrhagic telangiectasia (HHT, Osler-Weber-Rendu disease) is a systemic disorder of blood vessels. The most common manifestation of HHT is recurrent epistaxis, occurring in almost 90% of patients. Management of epistaxis is usually difficult and many types of treatment have been advocated. Of all these treatments, intranasal dermoplasty is considered the most effective one. It reduces the frequency of epistaxis by removing the telangiectatic mucosa and replacing it with a split thickness skin graft. We report a 55-year-old woman with HHT and recurrent epistaxis who was treated with intranasal dermoplasty. Postoperatively, she has shown considerable reduction in the frequency and severity of her epistaxis.