We herein report a case of pneumatosis intestinalis (PI), a condition characterized by the presence of gas within the wall of the digestive tract, associated with juvenile dermatomyositis (JDM). A 16-year-old girl, diagnosed with JDM at the age of 10, presented with abdominal pain and distention. She developed PI based on radiological findings that also included a dilated large intestine, extraluminal gas, and secondary diaphragmatic elevation. She was observed with medical therapy including bowel rest and hyperbaric oxygen therapy. However, she ultimately developed a strangulated obstruction 5 years after presentation with PI and large intestine resection and colostomy were performed emergently.
Miyamae, T., Ishiguro, N., Yonezawa, M., Tokushige, K., & Yamanaka, H. (2016). Pneumatosis Intestinalis Associated with Juvenile Dermatomyositis. Case Reports in Rheumatology, 2016, 1–4. https://doi.org/10.1155/2016/6497357