Double-outlet right ventricle

Abstract

Double-outlet right ventricle (DORV) defines malformation in which >50 % of each semilunar valve arises from the morphologic right ventricle (RV). It may coexist with any form of atrial situs or AV connections, and it is independent of conal anatomy. In the normal heart, conus which is a circular tube of muscle lies under the pulmonary valve, and the conus under the aortic valve is resorbed. In the DORV, variable amount of conal septum under the semilunar valves exist [1, 2].