Epidermolysis bullosa

Abstract

Inherited epidermolysis bullosa (EB) is a heterogeneous group of genodermatoses, due to defects in epithelial adhesion and characterized by the development of mucosal and cutaneous bullous lesions, after minimal traumas. The fragility of patients’ skin requires specific attention and care. The treatment varies upon the age of the patient, the subtype of EB, the level of systemic involvement, and the complications. Wound care is essential for exuding wounds, hyperkeratotic and crusted lesions, and infected wounds.