Ormond's disease.

Abstract

Three cases of Ormond's disease (syndrome) are described, and the aetiopathogenesis, clinical picture and diagnostics of the disease are dealt with in this report. Besides, the traditional therapy and the new therapeutic possibilities are discussed. For a disease of low incidence and assumed autoimmune origin malignancy cannot be excluded. Therefore, surgical exploration and histological verification are indispensable interventions in every case of Ormond's disease. In two of the present cases, steroid was administered in defence of percutaneous nephrostomy. In two cases, the recently recommended anti-oestrogen therapy was successful. Stagnation, or even regression, of the process followed. The authors are sure that they were the first in Hungary to administer anti-oestrogen to patients suffering from IFR.