Congenital pulmonary airway malformation

Abstract

Background: Congenital cystic adenomatoid malformations (CCAMs) are considered rare developmental anomalies of the lower respiratory tract. These are hamartomatous abnormalities of the lung with adenomatoid proliferation of cysts resembling bronchioles and usually occur sporadically and unilaterally with single lobe involvement. Method: A 6-year-old girl was admitted to our center because of prolonged fever and non-productive cough lasting3 months before admission. Results: The only other complaint was night sweating. She did not have dyspnea and did not mention any respiratory symptoms. On examination, coarse crackle and decreased lung sounds in the left side were detected. White blood cell count was 9.100/μL, hemoglobin was 11.2 g/dL, erythrocyte sedimentation rate was 50 and Creactive protein was 1+. IgA and IgM for hydatid cyst were tested and both were raised (14 and 1.4, respectively). Conclusion: The patient underwent surgery, with the probable diagnosis of hydatid cyst but in operating room diagnosis was changed and it was adenomatoid cystic malformation. In follow-up, she was in good general condition without any post-surgical complaints (Fig. 3, Ref. 11). Full Text in PDF www.elis.sk.