Left ventricular outflow tract obstruction secondary to right atrial dilatation and accessory mitral valve tissue in a patient with Ebstein’s anomaly- Case report

Abstract

Background: Ebsteins anomaly accounts for less than 1% of all congenital cardiac defects. Whilst typically characterised by dysfunction and anatomical defects of the right ventricle and tricuspid valve, it often co-exists with other congenital defects. Less frequently outflow tract obstruction may arise with associated haemodynamic effects and symptoms. In particular there are few reports in the literature of left ventricular outflow tract obstruction. We believe this is because symptomatic outflow tract obstruction as the presenting complaint of this condition is exceptionally rare.