Linear and whorled nevoid hypermelanosis

Abstract

A case of linear and whorled nevoid hypermelanosis is reported. The patient was a 17-year-old female and had pigmentary disorders since she was only two weeks after birth. The lesions were linear and whorled hyperpigmentation following the lines of Blaschko on the whole body except mucous membranes, eyes, palms, and soles. The skin biopsy revealed that increased pigmentation of the basal layer and increase of melanocytes without incontinence of pigments. This patient was diagnosed as linear and whorled nevoid hypermelanosis. This disease is often confused with other pigmented disorders, such as incontinentia pigmenti, early linear epidermal nevi.