Correlative imaging in an atypical case of Mazabraud syndrome

Abstract

Mazabraud syndrome is a rare phenomenon that reflects the association between intramuscular myxoma and fibrous dysplasia, which is usually polyostotic. Approximately 40 cases have been described in the literature since the initial report by Henschen [1] in 1926. Mazabraud et al. [2] in 1967 emphasized the association as part of the spectrum of fibrous dysplasia. We present an atypical example of the syndrome and the characteristic difficulties encountered in interpretation of correlative images that necessitated biopsy of the bone and soft-tissue components for a firm diagnosis. © American Roentgen Ray Society.