Pierre robin sequence

Abstract

The development of the accurate techniques for cephalometric roentgenography of infants has made possible a longitudinal study of the growth of the micrognathic mandible. As a result of these studies, useful diagnostic and prognostic information has been obtained to provide a rationale for the management of individual cases. The lateral cephalometric roentgenogram is a valuable diagnostic aid in assessing the severity of the glossoptosis and its obstruction of the airway. A definite correlation exists between the degree of constriction of the airway and the severity of the clinical state. On the basis of these findings, it is possible to recommend either conservative management or tracheotomy in extreme situations, or distraction osteogenesis. Three cases, out of a larger series of similar cases,were presented to indicate the spectrum of variations to be encountered. In all instances, it was found that where an adequate metabolic situation was provided and the infant gained weight, mandibular growth during the first few months was sufficient to provide for a natural resolution of the symptoms attending the glossoptosis. Longitudinal records have indicated that mandibular growth is proportionally adequate to reduce the retrognathic profile and provide an esthetically harmonious facial appearance. Based on investigations performed during the tenure of Special Research Fellowship from the National Institute of Dental Research Institutes of Health (Dr. Pruzansky, Senior Assistant Dental Surgeon [R], United States Public Health Service, National Institute of Dental Research, Department of Health, Education and Welfare). © 2006 Springer-Verlag Berlin Heidelberg.