Long-term results and quality of life after treatment of hirschsprung's disease and allied disorders

Abstract

The late follow-up of children with Hirschsprung's disease gives one the best opportunity to critically evaluate the efficacy and results of a particular surgical procedure. Unfortunately, most reviews of Hirschsprung's disease are hampered by the fact that follow-up periods are rather short and may not adequately reflect a patient's long-term outcome and lifestyle. In general, the most commonly encountered problems include constipation, incontinence, enterocolitis and the overall impact of the disease on lifestyle. Other complications, such as fistulae, obstructions and impotence are quite rare and are discussed toward the end of the chapter. Each of these problems is covered in the context of the four most commonly performed pull-through procedures: the Swenson, Duhamel and Soave (endorectal pull-through, ERPT, including the transanal route). The most recent technical modifications and literature reviews are included. © 2008 Springer-Verlag.