Prune belly syndrome

Abstract

Prune Belly Syndrome (PBS) is a rare anomaly of the anterior abdominal wall, urinary tract and undescended testes. It is thought to be caused by transient obstruction of the urethra between 10 and 20 weeks of gestation, leading to massive dilatation of the bladder which resolves in the third trimester. The atrophic abdominal wall and cryptorchidism are secondary to the enlarged bladder. Management primarily requires treatment of the intraabdominal testes.