Lethal Complications of the Ehlers—Danlos Syndrome

Abstract

Death from arterial bleeding or gastrointestinal perforation has previously been reported in more than 15 patients with the Ehlers-Danlos syndrome. On a basis of. 100 personally examined patients and a review of published accounts, these events seem particularly likely to occur in two distinct and recognizable forms (the gravis and the ecchymotic forms) of the syndrome. © 1968, British Medical Journal Publishing Group. All rights reserved.