Spontaneous biliary perforation, liver cysts, and abscesses

Abstract

This is a peculiar condition which seems limited to the first few weeks of life whereby perforation occurs in the extrahepatic bile duct typically leading to bile in the peritoneal cavity, abdominal distension and jaundice. It should be distinguished from spontaneous perforation in a pre-existing choledochal malformation, said to occur in about 5-10% of all large series.