Ebstein's malformation: Does echocardiographic assessment determine surgical repair?

Abstract

Ebstein's malformation is a complex lesion whose spectrum varies from the serious, when there is marked valvar dysplasia and deformity, to being relatively benign in nature. It is, therefore, impossible to provide a single option for treatment without understanding both the developmental aspects of this lesion and the fetal and neonatal presentations affecting not only the heart, but also other organs such as the lungs. An echocardiographer approaching this condition must take cognizance of many issues that are of critical importance when approaching the echocardiogram, which, while it cannot determine the repair on its own, is certainly a major determinant in deciding the type of repair needed.