Displasia ectodérmica hipohidrótica: Reporte de casos

Abstract

Ectodermal Hypohidrotic Dysplasia (EHD) is a genodermatosis characterized by the presence of the ectodermderived structures alterations and often the triad is given: Hypohidrosis, Hypotrichosis and hypodontia. The purpose of this article is to present 6 clinic cases attended in the Clinic of the Children Dental Care of the Faculty of dentistry of the University of Antioquia between 1998 and 2011. It's document the oral and facial characteristics in this pathology in a family with inheritance associated with the X chromosome. For the treatment of this syndrome a protocol of management in multidisciplinary and integral form is proposed.