Pulmonary atresia with intact ventricular septum

Abstract

It is important to employ a strategy for pulmonary atresia with intact ventricular septum (PAIVS) in collaboration with cardiology and cardiac surgery. We established our policy of treatment based on the right ventricular end diastolic volume. Sinusoidal communication should be carefully considered. Prognosis was poor in case of interruption of coronary arteries. Although catheter intervention is not fully established in initial treatment of PAIVS, it has a clinically significant roll in case of sufficient right ventricular end diastolic volume.