Lymphangiomas and Lymphangiomatosis

Abstract

Lymphangiomas are histologically benign but may have life-threatening potential with increasing size and encroachment of adjacent vital structures. Lymphangiomatosis is an extremely rare pathological condition where multiple lymphangiomas are present and may affect the visceral organs (lung, liver, and spleen), soft tissues, subcutaneous tissues, skin, and bones (long bones, pelvis, skull, vertebrae).