Introduction: Undifferentiated Liver Sarcoma, also known as Undifferentiated Embryonal Sarcoma of the Liver, is a rare, highly malignant neoplasm which affects mostly the pediatric population, although a few cases have been reported in adults. It accounts for about 13% of pediatric hepatic malignancies. Case presentation: We report a case of undifferentiated liver sarcoma in a 14-year-old Chinese boy who presented with non-specific right hypochondriac pain. Exploratory laparotomy with tumor resection was performed, followed by adjuvant chemotherapy. Conclusion: Undifferentiated Liver Sarcoma is a rare, highly malignant hepatic neoplasm affecting almost exclusively the pediatric population. The prognosis is poor but recent evidence shows that long-term survival is possible after complete surgical resection and postoperative chemotherapy. © 2008 Iqbal et al; licensee BioMed Central Ltd.
CITATION STYLE
Iqbal, K., Xian, Z., & Yuan, C. (2008). Undifferentiated liver sarcoma - Rare entity: A case report and review of the literature. Journal of Medical Case Reports, 2. https://doi.org/10.1186/1752-1947-2-20
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