Histological findings in the limb-muscle of two new cases of Rigid Spine Syndrome are described. The first male case exhibited a disproportion in fiber type with predominance of the type II fibers with a slight increase of large fibers. Some of the type I fibers were slightly atrophic. No other consistent abnormalities could be seen, excepted thickness of vessel basal lamina. The second female case had a relatively distinct muscular pattern. Necrotizing phenomenon were mild without fibrosis. Type I predominance were obvious. Atrophic and hypertrophic fibers could be seen in both types populations, with a relatively higher rate in type II. These two additional cases and those of the literature showed varied non specific histology, without any histo-chemical nor ultrastructural characteristic pattern.
CITATION STYLE
Mussini, J. M., Gray, F., Hauw, J. J., Piette, A. M., & Prost, A. (1981). Rigid spine syndrome: histological examinations of male and female cases. Acta Neuropathologica. Supplementum, 7, 331–333. https://doi.org/10.1007/978-3-642-81553-9_95
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