Bobble-head Doll Syndrome Associated with the III Ventricular Cyst: Three cases in children 7 years after CVP or CVA shunting

Abstract

Thirty-nine cases of the bobble-head doll syndrome have been operated upon and are described in the literature. The authors re-evaluate three cases of III ventricle cysts treated with cystoventriculoperitoneal (CVP) or cystoventriculoatrial (CVA) shunting 7 years ago. In the first case (a 4.5-year-old girl), the CVP shunt was removed after 16 months due to suppuration around the device after trauma of the scalp. Nevertheless, the communication between the ventricle and cyst continued and the bobbing never returned. In the second case (a 10-year-old girl), after 4.5 years a pseudocyst at the end of the peritoneal catheter was accidentally found. It was evacuated and, as in the third case (a 17-year-old boy) follow-up for 7 years showed excellent results from the clinical point of view and CT scans.