Double root translocation operation for complete transposition of great arteries with ventricular septal defect and pulmonary stenosis & double-outlet right ventricle with non-committed ventricular septal defect and pulmonary stenosis

Abstract

The abnormal connection of the ventricle and great arteries is a commonly seen congenital heart disease. It becomes even more clinically complicated when combined with pulmonary stenosis (PS) and ventricular septal defect (VSD). DORV with non-committed ventricular septal defect (DORVncVSD) represents the extreme end of DORV anatomical spectrum. There are problems for classic Rastelli (or REV) or Nikaidoh operations, such as long-term obstruction of left and right ventricle outflow tract and problems due to narrowing of the left ventricle to aorta tunnel. In 2004, double root translocation (DRT) was initially performed in Fuwai Hospital. It aims at retrieving the normal geometry of the left and right ventricle outflow tract, while at the same time maximally preserving function and growth potential of the aortic and pulmonary valves. Until May, 2013, 100 patients have undergone DRT operation in Fuwai Hospital and the early and late results were satisfactory.