Clinical presentation and therapy of hypoplastic left heart syndrome

Abstract

Hypoplastic left heart syndrome (HLHS) can result from a number of abnormalities that result in a very small, unusable left ventricle and severe hypoplasia of the ascending aorta. Theses abnormalities include aortic valve atresia or severe stenosis and/mitral valve atresia and/or stenosis without a ventricular septal defect (Fig. 55.1).