Phacomatosis pigmentopigmentalis: Aberrant mongolian spots and segmental café Au lait macules: Brief reports

Abstract

We report a case of an otherwise healthy male newborn, with segmental café au lait spots on his left buttocks and left thigh down to the medial knee, in a nevoid pattern, and an aberrant Mongolian spot on the ipsilateral cheek of the buttocks in a checkerboard pattern. We propose the name phacomatosis pigmentopigmentalis in analogy to phacomatosis pigmentovascularis, and phacomatosis pigmentokeratotica. © 2009 Wiley Periodicals, Inc.