Marfan syndrome

Abstract

A 33-year-old male patient with Marfan syndrome (MFS) presented for preoperative assessment before elective total thyroidectomy. One month prior to this presentation, he had undergone an uneventful aortic valve replacement (AVR) for severe aortic valve insufficiency and removal of Nuss bars. He had previously undergone an aortic valve-sparing root replacement and mitral valve repair, 15 and 8 years prior, respectively. He had a background of polymorphic ventricular tachycardia that required insertion of an implantable cardioverter-defibrillator (ICD). Day 1 post AVR, he developed rapid atrial fibrillation and decompensated heart failure requiring inotropic support. He was cardioverted successfully and started on amiodarone. One month later, he re-presented with amiodarone-induced hyperthyroidism.