Pulmonary hypertension associated with congenital heart disease, eisenmenger syndrome

Abstract

Obviously, the proper management of every disease needs the proper definition and classification. Pulmonary hypertension (PH) which is a hemodynamic and pathophysiological condition has been defined as raised mean pulmonary arterial pressure ≥25 mmHg at rest that is confirmed by right heart catheterization (RHC). PH has been found in multiple different clinical conditions, and the American and European guidelines have been provided a clear classification based on the pathophysiological mechanisms, clinical presentations, and therapeutic approaches (Table 15.1).