Supravalvular aortic stenosis

Abstract

Supravalvular aortic stenosis (sup AS) is the least common type of congenital left ventricular outflow tract (LVOT) obstruction. In the most common type of sup AS, there is a fixed aortic narrowing originating from just above the sinus of Valsalva which extends along a variable length of the aorta (hourglass type); the membranous type is the result of a fibrous or fibromuscular semicircular diaphragm with a small central opening in the lumen of the aorta, and diffuse hypoplasia of the ascending aorta illustrates the third type [1].