This paper describes data related to a research article entitled "Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF1 defects" . This paper includes data of the quantitative analysis of individual forms of respiratory chain complexes I, III and IV present in SURF1 knockout (SURF1-/-) and control (SURF1+/+) mouse fibroblasts and tissues and in fibroblasts of human control and patients with SURF1 gene mutation. Also it includes data demonstrating response of complex IV, cytochrome c oxidase (COX), to reversible inhibition of mitochondrial translation in SURF1-/- mouse and SURF1 patient fibroblast cell lines.
Kovářová, N., Pecina, P., Nůsková, H., Vrbacký, M., Zeviani, M., Mráček, T., … Houštěk, J. (2016). Data on cytochrome c oxidase assembly in mice and human fibroblasts or tissues induced by SURF1 defect. Data in Brief, 7, 1004–1009. https://doi.org/10.1016/j.dib.2016.03.065