An infant with beals-hecht syndrome: An airway challenge for the anaesthesiologist

Abstract

Beals-Hecht syndrome is a rare connective tissue disorder. Due to multiple contractures, it is associated with difficult airway and other anaesthesia related problems. We hereby present a case of a 2 month old infant who was scheduled for surgical repair of a large inguinal hernia. In view of the anticipated difficult airway, owing to the presence of micrognathia, limited mandibular excursion and cleft palate in this patient, we induced the child with sevoflurane maintaining spontaneous breathing and successfully intubated the child using video laryngoscope (Medicam paediatric video laryngoscope) with Miller blade size 0. Intraoperative course was uneventful, and the child was extubated at the end of surgery.