Visual loss and foveal lesions in Usher's syndrome

Abstract

Forty-eight patients with Usher's syndrome were assessed for the degree of visual loss, extent of lens opacities, and presence of foveal lesions. Twenty-one patients (44 %) showed either atrophic or cystic-appearing bilateral foveal changes. Despite having foveal lesions and variable degrees of lens opacities most patients maintained central visual acuity of 20/60 or better until their middle 30s.