Anestesia em paciente com distrofia muscular de Duchenne. Relato de caso

Abstract

BACKGROUND AND OBJECTIVES: Duchenne's Muscular Dystrophy is an X-linked recessive disorder, generally diagnosed in childhood, which progressively worsens to degenerate respiratory function. This report aimed at presenting the case of a patient with Duchenne's Muscular Dystrophy diagnosed 2 years before, submited to postectomy under genera anesthesia with ketamine S. CASE REPORT: Male patient, 9 years old, with Duchenne's Muscular Dystrophy diagnosed 2 years before, submitted to general anesthesia with intravenous levo-ketamine (1.5 mg·kg-1), under spontaneous ventilation manually assisted by Mapleson A Baraka system and penile block with 25 mg of 0.5% bupivacaine. Monitoring consisted of non invasive blood pressure, pulse oximetry, cardioscopy and esophageal temperature. There were no incidents during surgery, and after surgery patient had a few vomiting episodes, without other significant complications. Patient remained in hospital for 24 hours and was discharged asymptomatic. CONCLUSIONS: Very careful pre-anesthetic evaluation, adequate monitoring and drugs not predisposing to complications make surgery and postoperative period safe for Duchenne's Muscular Dystrophy patients.