Adult Chiari Type 1 Malformation with Holocord Syringomyelia Associated with Sagittal Synostosis

Abstract

Aim: to present evidence for the use of endoscopic third ventriculostomy (ETV) in the treatment of holocord syrinx. Methods: ETV has been used in the treatment of obstructive hydrocephalus and syringomyelia secondary to Chiari 1 malformation. However, there have been no reports of ETV being utilised in the management of a holocord. We report a case of an 18 year old male with a symptomatic holocord syrinx who was successfully treated via ETV. Results: neurological improvement was noted both immediately and at follow up following ETV. Conclusion: ETV may represent a viable treatment option for holocord syrinx in some population groups.