Orbital involvement in multifocal fibrosclerosis

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Abstract

Multifocal fibrosclerosis is a condition of unknown aetiology, characterised by fibrous lesions occurring at a variety of sites. Clinical variants include retroperitoneal fibrosis, Riedel's thyroiditis, sclerosing cholangitis, and mediastinal fibrosis. Orbital pseudotumour has been reported as a manifestation of this condition. Three patients with multifocal fibrosclerosis in whom orbital involvement was the dominant feature are described.

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Aylward, G. W., Sullivan, T. J., Garner, A., Moseley, I., & Wright, J. E. (1995). Orbital involvement in multifocal fibrosclerosis. British Journal of Ophthalmology, 79(3), 246–249. https://doi.org/10.1136/bjo.79.3.246

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