Pseudoxanthoma elasticum-like papillary dermal elastolysis

Abstract

Pseudoxanthoma elasticum-like papillary dermal elastolysis is a rare acquired idiopathic non-inflammatory elastolytic disorder. The skin lesions clinically resemble pseudoxanthoma elasticum but histopathologically there is elastolysis of the papillary dermis and there is no systemic involvement. We report the clinicopathological features of a 67-year-old female with this relatively newly described entity and discuss the pathogenesis, differential diagnosis and controversy regarding nomenclature.